Publications

Generation of Infectious Prions Amenable to Site-specific Click Chemistry.
Campbell RG, Iseler JN, Schwind AM, Supattapone S
bioRxiv. 2026 Apr 10; pii: 2026.04.08.717205. doi: 10.64898/2026.04.08.717205. Epub 2026 Apr 10.
PMID: 41993530

Energy Flux Regulates Cell Death Induced by California Serogroup Orthobunyaviruses.
Francomacaro LM, Matey H, Beauchemin KS, Evans AB, Supattapone S
bioRxiv. 2026 Mar 14; pii: 2026.03.13.711679. doi: 10.64898/2026.03.13.711679. Epub 2026 Mar 14.
PMID: 41958990

Mutant knock-in mice display enhanced susceptibility to pure prion protein fibrils.
Walsh DJ, Standke H, Kraus A, Watts JC, Supattapone S
J Gen Virol. 2026 Feb;107(2) doi: 10.1099/jgv.0.002219.
PMID: 41642644

Genome-wide screens identify core regulators of cell surface prion protein expression.
Beauchemin KS, Supattapone S
Sci Rep. 2026 Jan 21;16(1):5895. doi: 10.1038/s41598-026-37137-2. Epub 2026 Jan 21.
PMID: 41565761

Oligosaccharyltransferase (OST) complex inhibition effectively treats rodent and human prions.
Beauchemin KS, Kun J, Groveman B, Williams K, Salerno F, Francomacaro LM, Robison P, Haigh CL, Supattapone S
PLoS Pathog. 2026 Jan;22(1):e1013867. doi: 10.1371/journal.ppat.1013867. Epub 2026 Jan 12.
PMID: 41525337

Genome-Wide Screens Identify Core Regulators of Cell Surface Prion Protein Expression.
Beauchemin KS, Supattapone S
bioRxiv. 2025 Dec 9; pii: 2025.12.07.692843. doi: 10.64898/2025.12.07.692843. Epub 2025 Dec 9.
PMID: 41427295

Convergent generation of atypical prions in knockin mouse models of genetic prion disease.
Mehra S, Bourkas ME, Kaczmarczyk L, Stuart E, Arshad H, Griffin JK, Frost KL, Walsh DJ, Supattapone S, Booth SA, Jackson WS, Watts JC
J Clin Invest. 2024 Aug 1;134(15) doi: 10.1172/JCI176344. Epub 2024 Aug 1.
PMID: 39087478

Anti-prion drugs do not improve survival in novel knock-in models of inherited prion disease.
Walsh DJ, Rees JR, Mehra S, Bourkas MEC, Kaczmarczyk L, Stuart E, Jackson WS, Watts JC, Supattapone S
PLoS Pathog. 2024 Apr;20(4):e1012087. doi: 10.1371/journal.ppat.1012087. Epub 2024 Apr 1.
PMID: 38557815

Correction: Emergence of Prions Selectively Resistant to Combination Drug Therapy.
Burke CM, Mark KMK, Kun J, Beauchemin KS, Supattapone S
PLoS Pathog. 2024 Jan;20(1):e1011919. doi: 10.1371/journal.ppat.1011919. Epub 2024 Jan 8.
PMID: 38190351

Anti-prion drugs do not improve survival in knock-in models of inherited prion disease.
Walsh DJ, Rees JR, Mehra S, Bourkas MEC, Kaczmarczyk L, Stuart E, Jackson WS, Watts JC, Supattapone S
bioRxiv. 2023 Sep 29; pii: 2023.09.28.559951. doi: 10.1101/2023.09.28.559951. Epub 2023 Sep 29.
PMID: 37808761

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